Klippel-Trenaunay syndrome: Diagnosis and management
ZHANG Jian
Abstract：Klippel-Trenaunay syndrome (KTS) is a rare, complex malformation characterized by the clinical triad of capillary malformations (port wine stain), soft tissue and bone hypertrophy or hypotrophy of usually one lower limb occasionally and atypical lateral varicosity mostly. KTS is a mixed vascular malformation with predominant capillary, venous and lymphatic components, without significant arteriovenousshunting.Imaging before vascular interventions must confirm venous anatomy and deep venous drainage. Management is largely conservative. Compression is the hallmark of conservative management. laser can be used to treat port wine stains. Techniques for ablation of superficial veins and malformations are individualized. A multidisciplinary approach to management of KTS is warranted.
Keywords：Klippel-Trenaunay syndromeintralesion pho-to-coagulation
Publication Date：2015-01-01
Online Publishing Date：2025-08-15(First online date of this platform, not the publication date of the document)
Pages：4( 1298-1301 )