Cerebral hemispherectomy for Dyke-Davidoff-Masson syndrome:a case report
WANG Zhong-ming
XIE Qi
LU Jun
HUANG Ya-hui
WANG Qin
PENG Qiong
Abstract：Dyke-Davidoff-Masson syndrome(DDMS)is a rare central nervous system disorder characterized by varying degrees of hypoplasia or atrophy of one cerebral hemisphere,midline shift of the brain,and compensatory changes in the skull.This article reports a case of a 14-year-old female patient with DDMS who was admitted due to recurrent episodes of loss of consciousness and limb convulsions for 13 years following a craniocerebral injury.The patient exhibited normal muscle strength and tone in the right limbs,while the left upper limb showed proximal muscle strength of grade 3 and distal muscle strength of grade 2,and the left lower limb showed proximal muscle strength of grade 4 and distal muscle strength of grade 2,with normal muscle tone in the left limbs and a left hemiplegic gait.After non-invasive initial evaluations including MRI,PET,and VEEG,the patient underwent peri-insular hemispherotomy.Postoperatively,the wound healed well,the patient remained conscious,and muscle strength in the left limbs decreased.During the one-year follow-up after discharge,no epileptic seizures occurred,functional compensation was satisfactory,and no relatively severe complications were observed,achieving Engel ClassⅠoutcome.
Keywords：Dyke-Davidoff-Masson syndromeHemispherotomyEfficacy
Publication Date：2025-07-25
Online Publishing Date：2025-09-28(First online date of this platform, not the publication date of the document)
Pages：3( 440-442 )