A primary epithelioid sarcoma of the right lateral ventricle in an adult
LUO Deng-jian
HAN Feng
YANG Ming
YANG Hua
WAN Hao-jie
HUANG Rui
CHEN Wei
Abstract：Epithelioid sarcoma(ES)is a rare and highly aggressive malignant soft tissue neoplasm characterized by indolent,painless growths typically manifesting in the distal extremities of the limbs.These lesions are frequently misdiagnosed as benign entities.However,ES exhibits a pronounced predilection for local recurrence and propensity for lymphatic and hematogenous dissemination,resulting in an unfavorable prognosis.Primary ES originating within the central nervous system(CNS)is exceedingly uncommon,with clinical and radiological features lacking specificity,thereby posing diagnostic challenges that may lead to misidentification and delayed intervention.This report details a 60-year-old male presenting with a one-week history of declining memory function.Physical examination revealed no discernible abnormalities.Brain MRI showed a nodular lesion measuring approximately 1.8 cm×1.6 cm in the trigone of the right lateral ventricle,displaying prolonged T1 and slightly protracted T2 signal characteristics with conspicuous enhancement following contrast administration.Following thorough preoperative preparations,a complete resection of the lesion in the right lateral ventricle was achieved via the temporal lobe cortex approach.The postoperative pathological diagnosis confirmed ES.The patient did not undergo adjuvant radiotherapy or chemotherapy postoperatively.A follow-up was conducted 1.5 years after the surgery,and no tumor recurrence or distant metastasis was observed.Additionally,there were no positive neurological signs.
Keywords：Ventricular tumorsEpithelioid sarcomaMicrosurgery
Publication Date：2024-04-25
Online Publishing Date：2025-08-15(First online date of this platform, not the publication date of the document)
Pages：3( 251-253 )