Manifestations and Treatments of Hearing and Speech in Patients with Delayed Dominant Hereditary Sensorineural Deafness
Li Fude
CHEN Jiaping
ZHOU Xiangning
Abstract：To investigate the condition of the hearing and speech in subjects from 2 families with delayed dominant hereditary sensorineural deafness. Methods: The investigation of deafness heredity and the examination of systemic audiology were made in the 2 families. Results: The examination of pure tone hearing threshold showed that hearing threshold in all frequency ranges were severely elevated, the curve of hearing threshold revealed the descending type in 6 cases of the 2 families,among whom there were only residual hearings at low frequency in 3 ears of 2 cases,The ages of onset of hearing loss of the 2 families have some characteristics: the onset became younger, the course was shorter, the degree of deafness was worse from generation to generation. The earlier the onset of hearing loss was,the worse the speech function was. Conclusion:Ge
netic counseling and health education are important in reducing incidence of hereditary hearing loss. Hearing monitoring should be carried out periodically for children with history of hereditary hearing loss in their families. Hearing aids should be prescribed for probands as soon as hearing loss is verified. Speech rehabilitation is also advised when indicated.
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Publication Date：2001-01-01
Online Publishing Date：2025-08-15(First online date of this platform, not the publication date of the document)
Pages：3( 12-14 )