Clinical analysis of 16 cases with infantile Kasabach-Merritt syndrome
Abstract：Objective To investigate the clinical characteristics, diagnosis and treatment of infantile Kasabach-Merritt syndrome (KMS). Methods Sixteen infants diagnosed as KMS were collected in Beijing Children’s Hospital of Capital Medical University from Jan. 2008 to Dec.2014, and the clinical data of them were studied retrospectively. Results There were 7 male and 9 female. The average age was 75.8 days. The common clinical manifestations were thrombocytopenic consumption coagulopathy associated with enlarging hemangioma, which found on birth or shortly after birth. The therapy of all the patients were based on corticosteroid, supplemented with supportive treatments, 9 cases took regional injection or vascular embolization. Conclusions KMS onset early and in a critical condition. Comprehensive treatment would be taken to alleviate the condition of the illness. Corticosteroids are still preferred effective therapeutic agents. Treatment effect is good for most cases.
Keywords：Kasabach-Merritt syndromeAngiomaAnalysisclinical
Publication Date：2015-01-01
Online Publishing Date：2025-08-15(First online date of this platform, not the publication date of the document)
Pages：3( 257-259 )